Systemic Lupus Erythematosus (SLE)
Considerations
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Potential difficult airway but usually NOT an issue:
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C-spine arthritis
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Cricoarytenoid arthritis
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Recurrent laryngeal nerve palsy
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Multisystem complications of SLE:
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CNS: central & peripheral sensorimotor & autonomic neuropathies, seizure, stroke, mood, confusion, organic disease, transverse myelitis
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Cardiovascular: pancarditis with myocarditis (conduction disease, CHF), pericarditis (effusions/tamponade), non-infectious endocarditis (aortic & mitral regurgitations), accelerated coronary disease, hypertension, pulmonary hypertension
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Pulmonary: restrictive lung disease (ILD, pleuritis, effusions), pulmonary hypertension/RV failure, infection, pulmonary hemorrhage
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Renal: lupus nephritis, CRF
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Hematology: antiphospholipid-Ab syndrome common, risk of thromboembolism, anemia, thrombocytopenia, leukopenia factor deficiency (VIII, IX, XII) with implications for regional anesthesia
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Liver dysfunction can occur
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MSK: vasculitis, arthritis, joint immobility, migratory polyarthritis
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Medications:
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Steroids (Cushings/hyperglycemia/adrenal suppression/need for stress dose)
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Immunosuppresants/antimalarials
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NSAIDs
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Anticoagulants/ASA
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Potential for acute exacerbation with surgery, stress, infection & pregnancy
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Obstetric & cardiac anesthesia, especially in those with aPL antibodies or APS, requires multidisciplinary management at a specialist center
Pregnancy Considerations
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↑ risk of preterm labour & intrauterine fetal death
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Multidisciplinary management: rheumatology, obstetrics, anesthesia
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Potential coagulopathy may contraindicate use of neuraxial → ensure early hematology consult
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↑ PTT can have 2 causes:
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Presence of lupus anticoagulant: just a lab abN so clinically ok for neuraxial, these patients can actually be hyper-coagulable
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Autoantibodies against specific coagulation factors (e.g., VIII, IX, XII): risk of true coagulopathy → neuraxial contraindicated
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Document any pre-existing central or peripheral sensorimotor & autonomic neuropathies prior to regional technniques
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Potential for neonatal lupus & congenital heart block